Comprehensive Dental Rehabilitation of a Patient with Williams-Beuren Syndrome - A Case Report

Abstract

Williams-Beuren Syndrome (WBS) is a rare congenital disorder inherited on an autosomal dominant pattern. These patients often present with dysmorphic craniofacial features in addition to supravalvular aortic stenosis and cognitive impairment affecting their wellbeing. Unfortunately, the literature is sparse on the dental management of these patients. This case reports describes a patient with WBS who presented with the associated dento-facial characteristics. This report also outlines the interdiscliplinary dental management of the patient through combined orthodontic–orthognathic surgery – restorative procedures.